THE MUSCULAR DYSTROPHY OF THE BECKER (DMB) MUSCULAR DYSTROPHY BELONGING TO THE DISTROFINOPATIE GROUP, OF WHICH DUCHENNE MUSCULAR DYSTROPHY (DMD) IS IN THE FORM OF A SERIOUS IP. DISTROFINOPATIE IS CAUSED BY DISTRACTED MUTATIONS OF THE DYSTROPHIN GENE, A KEY PROTEIN FOR THE STABILISATION OF MUSCULO-SKELETAL FIBRES INTO SKELETAL FIBRES. DMB IS A RARE DISEASE, DIAGNOSED IN 10 TO 30 YEARS OF ET, WHICH AFFECTS MALES, WITH INCIDENCE D